Case Report Circumscribed juvenile pityriasis rubra pilaris
نویسندگان
چکیده
Pityriasis rubra pilaris (PRP) is an uncommon papulosquamous inflammatory dermatosis of unclear aetiology. Its most remarkable clinical findings are palmoplantar hyperkeratosis, orange-red scaling plaques and hyperkeratotic follicular papules. Its extension may vary from localised subtypes to generalised skin involvement with well-demarcated areas of spared skin ("islands of sparing") to erythroderma. Griffiths' classification is used to distinguish PRP in five clinical subtypes. Diagnosis is based on clinical and histopathological findings. The main differential diagnosis in a patient with circumscribed juvenile PRP (type IV) is psoriasis although keratosis pilaris, lichen spinulosus and follicular ichthyosis must also be ruled out. Treatment of pityriasis rubra pilaris remains a controversial topic due to the lack of large-scale clinical randomised trials and its unpredictable spontaneous resolution.
منابع مشابه
Circumscribed juvenile Pityriasis Rubra Pilaris associated with hypoparathyroidism and Brachyonychia: A case report
Circumscribed juvenile pityriasis rubra pilaris (PRP) is a form of PRP that manifests with well-defined erythematous scaly plaques with follicular keratosis mainly over knees and elbows. There are several reports of the association of PRP with other conditions. We report a boy with scattered erythematosquamous skin lesions and follicular hyperkeratotic papules since the age of six years. ...
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Pityriasis rubra pilaris is an uncommon inflammatory dermatosis that is well recognized across the globe. Erythroderma is a common presentation. A precise diagnosis of pityriasis rubra pilaris is based on morphologic features and is classified into 6 types: classic adult onset (type I), atypical adult (type II), classic juvenile (type III), circumscribed juvenile (type IV), atypical juvenile (t...
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Pityriasis rubra pilaris (PRP) has always been an intriguing topic ever since its inception. It is a group of chronic disorders characterized by reddish orange plaques with pityriasiform scaling showing follicular keratoses, palmoplantar keratoderma, and sometimes, erythroderma. It occurs all over the world but with racial variations. Its incidence might vary and the age at onset, behavior, cli...
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